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A clinical case of surgical treatment of lymphangioma at a difcult anatomical location in a 2-year-old child
- Authors: Poddubniy I.V.1,2, Trunov V.O.1,3, Tolstov K.N.1,2, Mager A.O.2
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Affiliations:
- Federal Scientific and Clinical Center for Children and Adolescents of FMBA of Russia
- A.I. Yevdokimov Moscow State University of Medicine and Dentistry
- Pirogov Russian National Research Medical University
- Issue: Vol 25, No 5 (2021)
- Pages: 341-345
- Section: CASE REPORT
- Submitted: 16.11.2021
- Accepted: 16.11.2021
- Published: 16.11.2021
- URL: https://jps-nmp.ru/jour/article/view/380
- DOI: https://doi.org/10.55308/1560-9510-2021-25-5-341-345
- ID: 380
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Abstract
Introduction. Lymphatic malformations are relatively rare in childhood. Their occurrence depends on age and varies between 1/600000 to 1/2500000. By literature data , the only radical curative option for this pathology is surgery; however, the relapse rate amounts to 25%. Therefore, further studies on the management of this pathology are needed.
Purpose. to present a rare clinical case of successful surgical treatment of a child with lymphatic mesentery malformation of the small intestine.
Materials and methods. The authors discuss various approaches to therapy and surgical care; they also present modern literature data and discuss the relevance of sclerosing preparations for injections directly into the cystic cavity. A clinical case of 2-year-old child with lymphangioma of complex anatomical location is described. The authors analyze ways of surgical intervention, early postoperative course and correction of the developed complications.
Results. Follow-up data were analyzed; the obtained results confrm a radical type of the performed surgery without worsening the quality of life.
Conclusion. Lymphangiomas at diffcult anatomical locations require a special attention during examination and treatment; radical removal can be considered as an effective option for treating such children.
About the authors
I. V. Poddubniy
Federal Scientific and Clinical Center for Children and Adolescents of FMBA of Russia; A.I. Yevdokimov Moscow State University of Medicine and Dentistry
Author for correspondence.
Email: fake@neicon.ru
ORCID iD: 0000-0002-9077-6990
115409, Moscow, Russian Federation
127473, Moscow, Russian Federation
РоссияV. O. Trunov
Federal Scientific and Clinical Center for Children and Adolescents of FMBA of Russia; Pirogov Russian National Research Medical University
Email: trunov2000@mail.ru
ORCID iD: 0000-0002-7568-4297
Vladimir О. Trunov – MD, Cand.Sc.(med), associate professor at the chair of pediatric surgery; Deputy Director
115409, Moscow, Russian Federation
117997, Moscow, Russian Federation
РоссияK. N. Tolstov
Federal Scientific and Clinical Center for Children and Adolescents of FMBA of Russia; A.I. Yevdokimov Moscow State University of Medicine and Dentistry
Email: fake@neicon.ru
ORCID iD: 0000-0003-2412-414X
115409, Moscow, Russian Federation
127473, Moscow, Russian Federation
РоссияA. O. Mager
A.I. Yevdokimov Moscow State University of Medicine and Dentistry
Email: fake@neicon.ru
ORCID iD: 0000-0002-2498-0184
127473, Moscow, Russian Federation
РоссияReferences
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