Systemic arterial blood supply in the spectrum of bronchopulmonary vascular malformations



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Abstract

Introduction. Congenital bronchopulmonary vascular malformations manifest a wide range of disorders in the three main components of the lungs: respiratory tract and lung parenchyma, arteries and veins. Malformations of all the main components of lung tissues, namely, arterial blood supply, venous outflow and respiratory tract - may be variants of a single primary complex of pulmonaryvascular anomalies.
Observation. A described clinical case demonstrates an extremely interesting mixed bronchoarteriovenous malformation affecting the pulmonary respiratory tract, pulmonary artery and pulmonary vein. Various instrumental techniques were used for the diagnostics, the key of which was computed tomography with intravenous contrast.
Conclusion. The article presents a wide range of pathological changes observed in this clinical case; it also analyzes the nature of each component and terminology.

About the authors

A. L. Yudin

Pirogov Russian National Research Medical University

Email: fake@neicon.ru
ORCID iD: 0000-0002-0310-0889

Moscow, 117997

Russian Federation

A. Yu. Razumovskiy

Pirogov Russian National Research Medical University; Filatov Children’s City Clinical Hospital

Email: fake@neicon.ru
ORCID iD: 0000-0002-9497-4070

Moscow, 117997

Moscow, 123001

Russian Federation

O. A. Afukova

Pirogov Russian National Research Medical University

Author for correspondence.
Email: afukova.oa@mail.ru
ORCID iD: 0000-0001-5562-6324

Olga А. Afukova, associate professor, department of radiation diagnostics and therapy 

Moscow, 117997

Russian Federation

Yu. A. Abovich

Pirogov Russian National Research Medical University

Email: fake@neicon.ru
ORCID iD: 0000-0002-9446-2163

Moscow, 117997

Russian Federation

E. A. Yumatova

Pirogov Russian National Research Medical University

Email: fake@neicon.ru
ORCID iD: 0000-0002-6020-9434

Moscow, 117997

Russian Federation

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