Achalasia of the cardia in Allgrove syndrome in an 8-year-old child



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Abstract

Introduction. The authors present a clinical case of an 8-year-old patient with an extremely rare Allgrove’s syndrome and cardia achalasia. By various authors, in case of this syndrome, achalasia of the cardia is diagnosed in 75% of cases, along with other symptoms. Currently, there are a number of modalities for treating achalasia of the cardia. However, the most popular one is cardiomyotomy by Heller in combination with fundoplication by Dor which recently has been successfully performed with minimally invasive laparoscopic techniques.
Clinical case. In present case, the patient had all possible minimally invasive surgical interventions. However, all attempts to apply organ-preserving techniques for treating achalasia of the cardia had failed .
Results. Finally, the child had esophageal plastic surgery – coloesophagoplasty with good clinical outcomes.

About the authors

A. Yu. Razumovsky

N.I. Pirogov Russian National Research Medical University; N.F. Filatov City Children’s Hospital

Author for correspondence.
Email: fake@neicon.ru
ORCID iD: 0000-0003-3511-0456

Moscow, 117997

Moscow, 103001

Россия

Z. B. Mitupov

N.I. Pirogov Russian National Research Medical University; N.F. Filatov City Children’s Hospital

Email: dr.mitupow@yandex.ru
ORCID iD: 0000-0002-0016-6444

 Zorikto В. Mitupov, MD, Dr.Sc.(med)

Moscow, 117997

Moscow, 103001

Россия

A. B. Alkhasov

N.I. Pirogov Russian National Research Medical University

Email: fake@neicon.ru
ORCID iD: 0000-0002-0644-2198

Moscow, 117997

Россия

D. M. Chubko

N.I. Pirogov Russian National Research Medical University

Email: fake@neicon.ru

Moscow, 117997

Россия

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