A successful treatment of total colonic aganglionosis in a child

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Introduction. The earliest mention of total colonic aganglionosis, as the form of Hirschsprung’s disease, is dated 1926. According to various sources, total colonic aganglionosis is met approximately in 1 per 500 000 live births. Currently, the curative strategy in total colonic aganglionosis is strongly personalized. There are various surgical techniques for managing this severe congenital colon anomaly. Recent achievements in pediatric coloproctology have minimized the mortality rate in children with intestinal neuronal dysplasia and total colonic aganglionosis. However, despite of the evident progress in coloproctology, questions about the volume of reconstructive surgery in total colonic aganglionosis, application of “reservoir” surgical techniques so as to promote child’s further development and socialization are still unsolved.
Material and methods. The patient was successfully treated with a reservoir technique which included an ileo-transverse anastomosis by Martin-Kimur with the formed conduit pulled to the anterior abdominal wall. Then, a radical intervention was made which consisted of combined abdominoperineal transanal endorectal pull through (TEPT) of the ileo-transverse conduit/reservoir, of the resection of rudimentary colon and a coloanal anastomosis by Boley.
Conclusion. The obtained small intestine-colon reservoir in total aganglionosis allows to preserve motor function due to peristaltic movements of the small intestine wall and to prevent intestinal obstruction, thereby facilitating the physiological function of the intestine. In addition, the colon wall in the reservoir saves the area of absorbing surface and minimizes water-electrolyte disorders.

作者简介

N. Stepanova

Irkutsk State Medical University; Irkutsk Municipal Pediatric Clinical Hospital

编辑信件的主要联系方式.
Email: sergiklee@mail.ru
ORCID iD: 0000-0001-5821-7059

Natalia M. Stepanova, Dr., chair of pediatric surgery, Irkutsk State Medical University

664003, Irkutsk
664009, Irkutsk

俄罗斯联邦

V. Novozhilov

Irkutsk State Medical University; Irkutsk Municipal Pediatric Clinical Hospital

Email: fake@neicon.ru
ORCID iD: 0000-0002-9309-6691

664003, Irkutsk
664009, Irkutsk

俄罗斯联邦

D. Zvonkov

Irkutsk Municipal Pediatric Clinical Hospital

Email: fake@neicon.ru
ORCID iD: 0000-0002-7167-2520

664009, Irkutsk

俄罗斯联邦

A. Voropaeva

Irkutsk State Medical University; Irkutsk Municipal Pediatric Clinical Hospital

Email: fake@neicon.ru
ORCID iD: 0000-0001-6709-3123

664003, Irkutsk
664009, Irkutsk

俄罗斯联邦

E. Petrov

Irkutsk Municipal Pediatric Clinical Hospital

Email: fake@neicon.ru
ORCID iD: 0000-0002-1083-0951

664009, Irkutsk

俄罗斯联邦

O. Оbarchuk

Irkutsk Municipal Pediatric Clinical Hospital

Email: fake@neicon.ru
ORCID iD: 0000-0002-5541-7335

664009, Irkutsk

俄罗斯联邦

D. Mikhailovskaya

Irkutsk Municipal Pediatric Clinical Hospital

Email: fake@neicon.ru
ORCID iD: 0000-0003-3755-0009

664009, Irkutsk

俄罗斯联邦

参考

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  2. Морозов Д.А., Пименова Е.С. Диагностика и лечение болезни Гиршпрунга у детей в Российской Федерации, подготовка проекта федеральных клинических рекомендаций. Российский вестник детской хирургии, анестезиологии и реаниматологии. 2018; 8(1): 6–12.
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  4. Чубарова А.И., Костомарова Е.А., Мокрушина О.Г., Шумихин В.С. и соавт. Опыт диагностики и лечения пациентов с тотальным и субтотальным аганглиозом кишечника. Российский вестник детской хирургии, анестезиологии и реаниматологии. 2016; 6 (2): 26–35.
  5. Шелыгин Ю.А. Клинические рекомендации. Колопроктология. М.: ГЭОТАР-Медиа. 2015: 50–51.
  6. Ruttenstock E., Puri P. A meta-analysis of clinical outcome in patients with total intestinal aganglionosis. Pediatr. Surg. 2009; 25: 833–9.

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